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Mixed Connective Tissue Disease

Controversial: distinct disease or combination of several autoimmune diseases
  • Systemic sclerosis
  • Polymyositis
  • Rheumatoid arthritis
  • Systemic LE
 
Labs:
  • High titer IgG anti-U1 ribonuclear protein (U1 RNP) antibodies
 
May be complicated by:
  • Pericarditis
  • Pulmonary arteritis or PAH (pulmonary arterial hypertension)