Neurocutaneous Syndromes

Neurocutaneous syndromes primarily involve the ectodermal tissue of the brain and skin
 
Ectoderm forms 3 types
  • Neuroectoderm - neural tube
  • Surface ectoderm - epidermis (not dermis, which is connective tissue)
  • Neural crest - melanocytes, schwann cells
 
Doenças a explorar
Tuberous Sclerosis complex | EPILOIA
Incontinentia Pigmenti
 
  • Neurofibromatosis Type 2