Mechanism
Anti-Neutrophilic Cytoplasmic Antibodies
- 3 patterns
- Cytoplasmic (C-ANCA)
- Ab agains proteinase 3 (PR3)
- Granulomatosis with polyangiitis
- Correlates well with disease activity
- Perinucleas (P-ANCA)
- Ab agains myeloperoxidase
- Eosinophilic granulomatosis with polyangiitis, drug-induced, microscopic polyangiitis (MPA)
- Atypical (A-ANCA)
Diseases